Polyarteritis nodosa and related conditions
Polyarteritis nodosa and related conditions
M30 is a header (parent) code in the ICD-10-CM hierarchy. It is not billable for claim submission. Use one of the billable child codes listed below.
Billable codes in this category
Each of the codes below is billable. Choose the one that most accurately describes the patient's diagnosis.
M30.0 identifies classic polyarteritis nodosa (PAN), a systemic necrotizing vasculitis affecting medium-sized muscular arteries, distinct from microscopic polyangiitis and other related vasculitides.
Systemic necrotizing vasculitis with granuloma formation and obligate pulmonary involvement, corresponding to eosinophilic granulomatosis with polyangiitis (EGPA), formerly called Churg-Strauss syndrome.
M30.2 classifies juvenile polyarteritis — a pediatric-onset necrotizing vasculitis of medium-sized arteries that mirrors polyarteritis nodosa (M30.0) but occurs in children and adolescents.
M30.3 identifies Kawasaki disease — an acute systemic vasculitis affecting medium-sized arteries, classified under polyarteritis nodosa and related conditions in the musculoskeletal and connective tissue chapter.
M30.8 captures conditions that fall within the polyarteritis nodosa family but don't fit the more specific subcategories under M30 — its primary 'Applicable To' entry is polyangiitis overlap syndrome.
Inclusion & exclusion notes
Excludes 1 (mutually exclusive — never code together)
- microscopic polyarteritis (M31.7)