Systemic sclerosis [scleroderma]
Systemic sclerosis [scleroderma]
M34 is a header (parent) code in the ICD-10-CM hierarchy. It is not billable for claim submission. Use one of the billable child codes listed below.
Billable codes in this category
Each of the codes below is billable. Choose the one that most accurately describes the patient's diagnosis.
M34.0 identifies progressive systemic sclerosis (diffuse cutaneous systemic sclerosis), a systemic autoimmune connective tissue disease characterized by widespread fibrosis of the skin and internal organs, vasculopathy, and immune dysregulation.
M34.1 captures the limited form of systemic sclerosis defined by the combination of calcinosis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, and telangiectasia — collectively known as CR(E)ST or CREST syndrome.
M34.2 identifies systemic sclerosis (scleroderma) that is directly attributable to exposure to a drug or chemical agent, distinguishing it from idiopathic or progressive systemic sclerosis subtypes.
M34.9 captures systemic sclerosis (scleroderma) when the clinical record does not specify the subtype — whether diffuse, limited, drug-induced, or an organ-involvement variant.
Inclusion & exclusion notes
Excludes 1 (mutually exclusive — never code together)
- circumscribed scleroderma (L94.0)
- neonatal scleroderma (P83.88)